Ectodermal Dysplasia Syndrome with comprehensive Oral rehabilitation - A Case Report
Keywords:
Ectodermal dysplasia, Dental Aesthetics, Prosthetics, RehabilitationAbstract
Ectodermal dysplasia (ED) is a hereditary disorder characterized by abnormal development of ectodermal derivatives resulting in abnormal morphological as well as functional presentation ofsweat glands, scalp hair, nails, skin pigmentation, and craniofacial structures. Orofacial manifestation of the ectodermal dysplasia may varies according to their chromosomal inheritance pattern with most frequently reported ED syndrome is X-linked hypohidrotic dysplasia and women being the more affected.The oral feature of the syndrome include anodontia or hypodontia, hypoplastic conical teeth, underdevelopment of the alveolar ridges ,and extra oral feature are frontal bossing, depressed nasal bridge, protuberant lips, and hypotrichosis which results in compromised aesthetics as well as masticatory function. Dental appearance in ED patients is extremely important because it can affect their self-esteem and is also a feelgood factor for family members. Prosthodontics treatment of ED is extremely important to restore these function which includes fixed, removable, or implant supported prostheses.
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