Giant pleomorphic lipomatosis of upper back and axilla in an elderly female with genodermatosis A rare case report and review of literature

Abstract

Pleomorphic lipoma is a rare, benign, pseudosarcomatous, soft-tissue neoplasm that typically involves the subcutis of the posterior neck, upper back, and shoulders. Pleomorphic lipoma is a variant of spindle cell lipoma, and these two types of lipoma exhibit similar histological fea- tures and immunophenotypes. Rarely can it be cutaneous manifestation of a paraneoplastic syndrome. We report a case of long standing multiple lipomas in an elderly female with a rare genodermatoses (lamellar icthyosis). Presentation was of a wellcircumscribed subcutaneous mass. Associated functional limitation of the affected shoulder was seen. Complete surgical excision with acceptable cosmosis was achieved. Histopathology revealed pleomorphic lipoma.