Castlemans disease presenting as persistent asymptomatic cervical lymphadenopathy in a child: A very rare disease with atypical presentation

Abstract

Castlemans disease is a rare atypical lympho-proliferative disorder characterised by enlarged hyperplastic lymphnodes with striking vascular proliferations. A cervical location has very rarely been reported in paediatric literature. It can be unicentric or multicentric. There are mainly four histological variants, hyaline vascular type being the commonest one.Although unicentric Castleman's disease carries a favorable prognosis in children, surgical excision is recommended to confirm the diagnosis and to rule out other causes. We report a case of unicentric cervical Castlemans disease of neck in a 6-years old male child, who came to paediatric ward with history of right sided neck mass since 2yrs. After thorough clinical examination and investigations, complete excision of the mass was done. Histopathological examination confirmed the diagnosis of Castlemans disease-hyaline vascular type. On follow-up for two years no recurrence has been seen.