Hyalinizing Spindle Cell Tumour with Giant Rosettes (HSCTGR) - A sequelae neurofibromatosis

Authors

  • Nikhil S Shetty Assistant Professor, Department of General surgery, A.J Shetty Institute of Medical Sciences, Mangalore, Karnataka
  • Vijay P Agrawal Assistant Professor, Dept.of General surgery, NKPSIMS, LMH, Nagpur
  • Ashwin Narasimhaprasad Orthopaedic surgeon, Ashwini hospital, Hoskote, Bangalore

DOI:

https://doi.org/10.7439/ijbar.v6i4.1809

Abstract

Generalised neurofibromatosis (von Recklinghausens disease) 1:4000 birth is an inherited autosomal dominant disease wherein there will be multiple neuro fibromas in the body- Chromosome 17. Usual indication for excision is symptomatic neurofibroma-pain and pressure symptoms, cosmetically problematic lesion, recent increase in size, malignant transformation seen in 5 % cases. We present a very rare case- 66 year old male who underwent excision of a symptomatic neurofibroma over left popliteal joint. Three months post-operatively patient developed a fast growing tumour measuring 10 X 6 cm at the operated site. FNAC report revealed hyalinizing spindle cell tumour with giant rosettes (HSCTGR). The rarity of this tumor is demonstrated by the small number of cases available; to date, only 38 cases have been reported in the world literature.

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Author Biography

  • Vijay P Agrawal, Assistant Professor, Dept.of General surgery, NKPSIMS, LMH, Nagpur

    Assistant Professor, Department of General surgery,

    NKPSIMS, LMH, Nagpur.

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Published

2015-03-29

Issue

Vol. 6 No. 4 (2015): Apr

Section

Case Report

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How to Cite

Hyalinizing Spindle Cell Tumour with Giant Rosettes (HSCTGR) - A sequelae neurofibromatosis. (2015). International Journal of Biomedical and Advance Research, 6(4), 379-381. https://doi.org/10.7439/ijbar.v6i4.1809
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